In rheumatology, Behcet's Syndrome, or Behçet's Disease, is a rare chronic inflammatory disease involving the small blood vessels. It is of unknown etiology, although it may be an autoimmune disease and have genetic components.
The syndrome is characterized by mucocutaneous ulceration in the mouth and genital region, and uveitis with hypopyon. Recurrent oral ulcers are a key marker. Other symptoms include painful, stiff and swollen joints . The neuro-ocular form may cause blindness and death. Synovitis; thrombophlebitis; gastrointestinal ulcerations; retinal vasculitis;optic atrophy and meningitis may occur as well."
Hughes-Stovin Syndrome was diagnosed in the "The Down Low" in season 6, episode 10 of the television series House.
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- Vedat Hamuryudan, et al. (15 March 1998), "[http://www.annals.org/content/128/6/443.full Thalidomide in the Treatment of the Mucocutaneous Lesions of the Behcet Syndrome A Randomized, Double-Blind, Placebo-Controlled Trial]", Ann Intern Med 128 (6): 443-450