Galactosidase
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In biochemistry, galactosidases are enzymes that are "a family of galactoside hydrolases that hydrolyze compounds with an O-galactosyl linkage."[1]
Classification
- alpha-galactosidase. Alpha-galactosidase A is the enzyme that is deficient in Fabry's Disease. Recombinant preparations of alpha-galactosidase A are agalsidase beta (Fabrazyme) and agalsidase alfa (Replagal). Beano® is an oral alpha-galactosidase.[2]
- beta-galactosidase. Beta-Galactosidase A1 enzyme deficiency may cause gangliosidosis. Lactase is a beta-galactosidase.
References
- ↑ Anonymous (2023), Galactosidase (English). Medical Subject Headings. U.S. National Library of Medicine.
- ↑ Banikazemi M, Bultas J, Waldek S, Wilcox WR, Whitley CB, McDonald M et al. (2007). "Agalsidase-beta therapy for advanced Fabry disease: a randomized trial.". Ann Intern Med 146 (2): 77-86. PMID 17179052.