Behcet's syndrome
Jump to navigation
Jump to search
In rheumatology, Behcet's Syndrome, or Behçet's Disease, is a rare chronic inflammatory disease involving the small blood vessels. It is of unknown etiology and characterized by mucocutaneous ulceration in the mouth and genital region, and uveitis with hypopyon. Other symptoms include painful, stiff and swollen joints [1]. The neuro-ocular form may cause blindness and death. Synovitis; thrombophlebitis; gastrointestinal ulcerations; retinal vasculitis;optic atrophy and meningitis may occur as well."[2]
A variation may be Hughes-Stovin Syndrome which is pulmonary artery aneurysms associated with systemic thrombosis.[3][4]
Notable cases
Hughes-Stovin Syndrome was diagnosed in the "The Down Low" in season 6, episode 10 of the television series House.
References
- ↑ http://www.nlm.nih.gov/medlineplus/behcetssyndrome.html
- ↑ Anonymous (2024), Behcet's syndrome (English). Medical Subject Headings. U.S. National Library of Medicine.
- ↑ Emad Y, Ragab Y, Shawki Ael-H, Gheita T, El-Marakbi A, Salama MH (2007). "Hughes-Stovin syndrome: is it incomplete Behçet's? Report of two cases and review of the literature.". Clin Rheumatol 26 (11): 1993-6. DOI:10.1007/s10067-007-0609-y. PMID 17457658. Research Blogging.
- ↑ Erkan D, Yazici Y, Sanders A, Trost D, Yazici H (2004 Jul-Aug). "Is Hughes-Stovin syndrome Behçet's disease?". Clin Exp Rheumatol 22 (4 Suppl 34): S64-8. PMID 15515789.